Wednesday, 7 May 2014

Chapter 4: Clinical picture and complications






         Asymptomatic CBD stones may be found incidentally during evaluation of patients with suspected gallstones. In fact, in non-jaundiced patients with normal ducts on trans-abdominal ultrasound the prevalence of CBD stones at the time of cholecystectomy is unlikely to exceed 5% (Collins et al., 2004).

         Patients with choledocholithiasis may present with biliary colic. The pain is usually located in the right upper quadrant and/or epigastrium and frequently radiates to the back and right scapula. The intensity of the pain is often severe enough that patients often seek immediate medical attention with the first episode. Classically, the pain of biliary colic occurs following fatty meals, although this situation does not occur in most cases. An association with meals is present in only 50% of patients, and in these patients, the pain often develops more than 1 hour after eating. In the remaining patients, the pain is not temporally related to meals and often begins at nighttime waking the patient from sleep.The duration of pain is typically 1 to 5 hours. The attacks rarely persist for more than 24 hours and are rarely shorter than 1 hour. It is not possible to differentiate between biliary colic due to cystic duct obstruction by gallbladder stones and biliary colic caused by stones migrated to the bile duct. In fact, the term “biliary colic” does not pretend to make such differentiation (Besselink et al., 2009). Pain is likely to be caused by distension of the bile duct by the offending stone(s) within the bile duct. The probability of stone retention increases with increasing diameter of the stone(s) (Festi et al., 1999).

            Other presenting symptoms include bilirubinuria (or tea-colored urine), pruritus, acholic stools, and jaundice. However, the biliary obstruction usually is incomplete. There may be nausea and vomiting with intermittent or constant epigastric or right upper quadrant (RUQ) pain. Typically, the pain and jaundice associated with CBD stones are more intermittent and transient than when the biliary obstruction is caused by a malignancy (Nakeeb 2006).

         Physical examination of patients with choledocholithiasis may be normal or reveal jaundice, scleral icterus, and abdominal tenderness over the right upper quadrant without peritoneal signs. Early in the course, physical examination may not be very different from that of patients with cholecystitis (Eisen et al., 2001).

The natural history of a given CBD stone is difficult to predict. In a prospective study of 1000 patients with symptomatic gallstones, it was found that 73% of cases that presented with features suggestive of CBD stones had no CBD stones at time of operation, and were therefore considered to have passed the stone spontaneously. However, cases of cholangitis or jaundice were less likely to pass stones spontaneously (Tranter 2003). In another study, the frequency of unexpected bile duct stones in patients who have experienced biliary colics varies between 5% and 12%.These data indicate that bile duct stones are relatively rare in patients with biliary colics and/or that most bile duct stones migrate spontaneously to the duodenum (Caddy et al., 2006).
 

The clinical course may be complicated by acute gallstone pancreatitis, cholangitis, or rarely, hepatic abscess. Also prolonged biliary obstruction can lead to biliary cirrhosis and portal hypertension (Ko et al., 2002).

CBD stones are covered by a bacterial biofilm of adherent quiescent bacteria residing in a hermetic environment. When stones cause obstruction of the ducts, cytokines released by epithelial cells activate these bacteria to the planktonic and virulent forms. Therefore, bile duct obstruction secondary to stones often is accompanied by bacterial sepsis resulting from activation of the bacterial biofilm on these stones. Sepsis is much less likely to occur in the context of malignant obstruction without choledocholithiasis (Ko et al., 2002).

The classical diagnostic presentation of cholangitis is Charcot’s triad which includes: jaundice, right hypochondrial tenderness and fever with chills. A consensus meeting was held in Tokyo in 2007 to define diagnostic criteria of acute cholangitis. Some panelists proposed that history of biliary disease should be included in the diagnostic criteria for acute cholangitis (Mayumi et al., 2007).

 

Table (1): diagnostic criteria for acute cholangitis (Mayumi et al., 2007).

A. Clinical context and clinical manifestations
 
1. History of biliary disease
2. Fever and/or chills
3. Jaundice
4. Abdominal pain (RUQ or upper abdominal)
B. Laboratory data
5. Evidence of inflammatory response[1]
6. Abnormal liver function tests[2]
C. Imaging findings
 
7. Biliary dilatation, or evidence of an etiology (stricture, stone, stent, etc)
Suspected diagnosis:
Two or more items in A
Definite diagnosis:
 
·        Charcot’s triad (2 + 3 + 4)
·        Two or more items in A + both items in B + C

 

              Gallstone pancreatitis can develop from the obstruction of the ampulla of Vater by common duct stones. CBD stones are responsible for up to 50% of all cases of pancreatitis.The risk of persistent ampullary obstruction increases with advanced patient age and stone size less than 5 mm (Telem et al., 2009). Most patients with gallstone pancreatitis experience a mild self-limited attack from which they recover within a few days; however, some patients will progress to develop severe pancreatitis with peripancreatic necrosis, infection, or pseudocyst formation. Severe tenderness may point to acute gallstone pancreatitis (Eisen et al., 2001). Persistent CBD stones may also increase acute biliary pancreatitis mortality rate. Autopsy studies demonstrate CBD stones in up to 60% of patients with mortality secondary to acute biliary pancreatitis (Telem et al., 2009).

        Some cases of acute biliary pancreatitis  are due to the biliary microcrystals (microlithiasis). The pathogenesis of acute pancreatitis produced by biliary crystals is unknown. It is probably related to the temporary impaction or migration of very small stones or clusters of crystals at the level of the ampulla of Vater. The mechanism of such pancreatitis is presumably the same as that when “normal size” biliary stones are impacted in the ampulla of Vater in the onset of the disease. However, most of patients presented with this condition suffered from acute pancreatitis classified in earlier litrautrue as so called “idiopathic” pancreatitis, as they do not bear gallbladder sludge, gallbladder stones and they did not have the history of cholecystectomy (Kohut et al., 2002).

Finally, prolonged biliary obstruction can lead to biliary cirrhosis. The average time for choledocholithiasis to lead to biliary cirrhosis is about 5 years, depending on the extent of obstruction. Even with cirrhosis, however, the obstruction should be relieved because some reversal of portal hypertension and secondary biliary cirrhosis may be possible (Ko et al., 2002).




[1] Abnormal WBC count, increased serum CRP level, and other changes indicating inflammation.
 
[2] Increased serum ALP, γ-GTP (GGT), AST, and ALT levels.
 

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